A Rare Presentation of Systemic Lupus Erythematosus with Leg Ulcers and Degos-Like Lesions
نویسندگان
چکیده
Degos-like lesions (DLL) have been associated with connective tissue diseases. Till date only twelve cases of systemic lupus erythematosus (SLE) DLL published. We describe a rare case SLE leg ulcers and DLL. A 23-year-old male presented malar rash, photosensitivity, ulcers, joint pain, oral altered sensorium dyspnea. Cutaneous examination also revealed atrophic, porcelain-white scars over body previously unnoticed by patient. Dermoscopy atrophic was pathognomonic Degos disease. Histopathology from various were consistent disease SLE. Patient admitted in intensive care unit but succumbed to multiorgan failure two days later. This highlights the importance dermoscopy for immediate diagnosis Appropriate investigations early timely management can decrease mortality. Also thorough diseases may reveal uncommon that alter clinical course outcome patients.
منابع مشابه
Degos-Like Lesions Associated with Systemic Lupus Erythematosus
Degos disease, also referred to as malignant atrophic papulosis, was first described in 1941 by Köhlmeier and was independently described by Degos in 1942. Degos disease is characterized by diffuse, papular skin eruptions with porcelain-white centers and slightly raised erythematous telangiectatic rims associated with bowel infarction. Although the etiology of Degos disease is unknown, autoimmu...
متن کاملIsolated thrombocytopenia report of a rare presentation of childhood Systemic Lupus Erythematosus
Background: Systemic lupus erythematosus (SLE) has various presentations in children. Hematologic abnormalities is common in childhood onset of SLE, however, isolated thrombocytopenia is relatively rare. Thus, we present a child with isolated thrombocytopenia as a rare presentation of SLE. Case presentation: A 12-year-old boy with chief complaints of loss of appetite, weight loss, decrease...
متن کاملSystemic Lupus Erythematosus with targetoid lesions: “Rowell Syndrome” or a rare manifestation of Lupus Erythematosus
Rowell syndrome is usually diagnosed by the presence of erythema multiforme like targetoid lesions in the patients of cutaneous or systemic lupus erythematosus and characterized by specific serological or immunological profile like speckled antinuclear antibody pattern, antibody against saline extract of human tissues (anti-SjT) and positive serum rheumatoid factor.The absence of a universally ...
متن کاملRare Association between Kikuchi's Disease and Systemic Lupus Erythematosus
Histiocytic necrotizing lymphadenitis or Kikuchi's disease is a rare, benign condition of unknown etiology, which is usually characterized by cervical lymphadenopathy and fever. This disease is rarely associated with systemic lupus erythematosus. Here we describe, for the first time in Iran, a patient who developed systemic lupus erythematosus about 3 years after the initial diagnosis of Kikuch...
متن کاملHypocomplementemic urticarial vasculitis: a rare presentation of systemic lupus erythematosus.
BACKGROUND Urticarial vasculitis is a small-vessel vasculitis, presenting clinically as persistent urticarial skin lesions and microscopically as leucocytoclastic vasculitis. Hypocomplementemic urticarial vasculitis syndrome (HUVS) is a distinct type of urticarial vasculitis with multiorgan involvement, whose etiology and link with other diseases are still unknown. Some authors have suggested t...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Turkiye Klinikleri Journal of Dermatology
سال: 2023
ISSN: ['1300-0330']
DOI: https://doi.org/10.5336/dermato.2022-92233